Epidermólise Bolhosa: Manejo das Coberturas

Abstract

Epidermolysis Bullosa is a rare disease, non-contagious and without cure, hereditary caused
by mutations in several previous skin proteins, of different intensities that can give rise to
flictenes throughout the body, the severity of which will depend on the mutation involved
in the pathogenesis. The four main types: simple, junctional, dystrophic and infantile. This
article aimed to evaluate the proper management, related to the use of coverings in the
patients with the disease. For this, a review of all specific literature found on the topic was
carried out. They were consulted as electronic bases scielo, bireme and Google Scholar
in the period of March and April 2021; in addition to primary sources such as books. The
material was selected according to the keywords: Epidermolysis Bullosa, causes, treatment,
use of coverings; data from 2010 to 2021. The results found show that the care provided
to patients with the disease, regardless of type, is nonspecific, with proper management of

skin lesions according to the characteristics being considered of great importance. A rigo-
rous assessment by the multidisciplinary team is recommended to analyze skin and extracu-
taneous involvement, avoiding complications such as, for example, guaranteeing a better

quality of life. It is concluded that the treatment of epidermolysis Bullosa should focus on the
prevention of complications, using appropriate coverage for each evolution of activities,
also involving the psychological care of the patient and family, for a better understanding of
the disease, thus resulting in better care.